Linear collagen naevus: an unusual connective tissue disorder.

© 2014 The Authors. doi: 10.2340/00015555-1747 Journal Compilation © 2014 Acta Dermato-Venereologica. ISSN 0001-5555 Connective tissue naevi are circumscribed skin lesions characterised by an increase or structural alteration of either collagen or elastin fibres (1). Collagen naevi occur in a patchy form as a feature of tuberous sclerosis, whereas elastin-rich naevi are noted in Buschke-Ollendorff syndrome. In both of these autosomal dominant traits, rather large lesions probably represent a type 2 segmental manifestation, being superimposed on the nonsegmental phenotype (2). By contrast, the linear collagen naevus tends to occur as a sporadic and isolated disorder (3, 4). Here we describe a further case of this unusual naevus.